Gastrointestinal Stromal Tumor in a Patient with Neurofibromatosis Type I: Diagnosis after Intestinal Occlusion Secondary to Adhesions after an Episode of Pancreatitis

نویسندگان

چکیده

Introduction: Gastrointestinal stromal tumors (GIST), although relatively rare, account for 80% of mesenchymal the digestive tract. They manifest in any part alimentary tract and are derived from Cajal cells. may occur sporadically or be associated with familial syndromes such as neurofibromatosis type I. The clinical picture is variable, they often diagnosed incidentally. diagnosis requires imaging tests histopathological immunohistochemical analysis. best strategy treatment surgical resection cases should analyzed individually to verify additional advantages association systemic therapy. This study aims present an unusual case GIST I a patient incidental after semi-intestinal occlusion secondary episode pancreatitis, addition performing literature review on subject. Case report: A 49-year-old woman history severe pancreatitis presented intestinal obstruction approximately 8 months this episode. Abdominal computed tomography revealed heterogeneous formation mesogastric region, measuring 6.6 x 5.1 5.3 cm. She underwent studies confirmed GIST. Six diagnosis, good general condition Conclusion: rare tumors, but their come mind patients 1 abdominal masses.

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ژورنال

عنوان ژورنال: Revista Brasileira de Cancerologia

سال: 2023

ISSN: ['0034-7116', '2176-9745']

DOI: https://doi.org/10.32635/2176-9745.rbc.2023v69n2.3720